Item type |
学術雑誌論文 / Journal Article(1) |
公開日 |
2011-01-14 |
タイトル |
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タイトル |
Conventional Diet Therapy for Hyperammonemia is Risky in the Treatment of Hepatic Encephalopathy Associated with Citrin Deficiency |
言語 |
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言語 |
eng |
DOI |
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関連識別子 |
https://doi.org/10.2169/internalmedicine.49.2712 |
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関連名称 |
10.2169/internalmedicine.49.2712 |
キーワード |
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主題 |
citrin deficiency, CTLN2, low protein diet, carbohydrate |
資源タイプ |
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資源 |
http://purl.org/coar/resource_type/c_6501 |
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タイプ |
journal article |
著者 |
Fukushima, Kazuhiro
Yazaki, Masahide
Nakamura, Mio
Tanaka, Naoki
Kobayashi, Keiko
Saheki, Takeyori
Takei, Hideki
Ikeda, Shu-ichi
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信州大学研究者総覧へのリンク |
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氏名 |
Yazaki, Masahide |
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URL |
http://soar-rd.shinshu-u.ac.jp/profile/ja.gpTauakh.html |
出版者 |
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出版者 |
JAPAN SOC INTERNAL MEDICINE |
引用 |
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内容記述 |
INTERNAL MEDICINE. 49(3):243-247 (2010) |
書誌情報 |
INTERNAL MEDICINE
巻 49,
号 3,
p. 243-247,
発行日 2010
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抄録 |
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内容記述 |
Citrin deficiency caused by SLC25A13 gene mutations develops into adult-onset type II citrullinemia (CTLN2) presenting with hepatic encephalopathy. Recent studies have suggested that excessive loading of carbohydrates is harmful in citrin-deficient individuals. Here we report a CTLN2 patient who showed further deterioration of encephalopathy after the employment of conventional low-protein diet therapy for chronic liver failure. Owing to the high carbohydrate content, the conventional low-protein diet therapy should be avoided in patients with hepatic encephalopathy associated with citrin deficiency. In addition, our observation may suggest that carbohydrate-restricted diet in which the content of carbohydrate is below 50% of daily energy intake can have therapeutic efficacy in CTLN2 patients. |
資源タイプ(コンテンツの種類) |
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内容記述 |
Article |
ISSN |
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収録物識別子タイプ |
PISSN |
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収録物識別子 |
0918-2918 |
書誌レコードID |
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収録物識別子タイプ |
NCID |
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収録物識別子 |
AA10827774 |
PubMed |
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関連識別子 |
https://pubmed.ncbi.nlm.nih.gov/20118603 |
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関連名称 |
20118603 |
権利 |
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権利情報 |
Copyright (c) 2010 The Japanese Society of Internal Medicine |
出版タイプ |
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出版タイプ |
VoR |
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出版タイプResource |
http://purl.org/coar/version/c_970fb48d4fbd8a85 |
WoS |
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URL |
http://gateway.isiknowledge.com/gateway/Gateway.cgi?&GWVersion=2&SrcAuth=ShinshuUniv&SrcApp=ShinshuUniv&DestLinkType=FullRecord&DestApp=WOS&KeyUT=000274319200008 |